Presented by David R. Spielberg, MD, MHSc, Texas Children’s Hospital, Houston, TX Often the pulmonary complications of the lymphatic malformations can manifest as or mimic other common disorders: cough or wheezing, thus mimicking asthma or non-specific chronic cough. Lack of response to the usual treatments for these disorders may be a clue to the presence of some other process. This
» Read morePresented by Yaser A. Diab, M.B.B.S., Children’s National Health System, Washington, DC Complex lymphatic anomalies including Generalized Lymphatic Anomaly (GLA), Gorham–Stout disease (GSD), and Kaposiform Lymphangiomatosis (KLA) can involve the bones leading to bone destruction which can negatively impact the quality of life for patients with these lymphatic anomalies. At present, no standard treatment for these diseases exist, and due
» Read morePresented by Cameron Trenor, MD, MMSc, Vascular Anomaly Center, Boston Children’s Hospital Sirolimus has been FDA-approved since 1999 for immunosuppression but has many appreciated off-label uses, including for lymphatic disorders. Based on clinical study results and reported cases, sirolimus is often used for Gorham-Stout disease (GSD), generalized lymphatic anomaly (GLA)/lymphangiomatosis and other lymphatic conditions. Many lymphatic malformations are associated with
» Read morePresented by Maxim Itkin, MD, Director, HUP/CHOP Center for Lymphatic Imaging and Interventions Abstract: Lymphatic malformations (LM) are conditions that are characterized by proliferation of the lymphatic tissue in multiple organs. The major cause of mortality and morbidity in patients with LM is deterioration of pulmonary function due to chronic chylous effusions and progressive interstitial lung disease. The etiology of
» Read morePresented by Matt Hawkins, MD, Director – Pediatric Interventional Radiology, Children’s Healthcare of Atlanta at Egleston; Medical Director – Vascular Anomalies Clinic, Children’s Healthcare of Atlanta; Assistant Professor – Emory University School of Medicine Dept of Radiology and Imaging Sciences Abstract: Diagnostic imaging has become the primary means by which a number of lymphatic anomalies are diagnosed. More specifically, recent
» Read moreUpdate: If you missed the webinar on August 28, it is available for viewing on the ATS website. August 24 – 30, 2014 For the third consecutive year, Lymphangiomatosis and Gorham’s disease are being featured as part of Rare Lung Disease Week at the ATS. The feature of the week occurs on Thursday, August 28 when the Lymphangiomatosis and
» Read moreLymphangiogram is a test very similar to a CT scan, except the contrast dye is injected into the lymphatic vessels. In this post we’ve included links to information about how the test is performed. It is not a commonly performed test, but some in the LGDA community have had it done. Of course, these articles about the test make no
» Read moreOur website is designed to help you learn about lymphangiomatosis and Gorham’s disease. We hope you find it easy to navigate and to find the information you are looking for. In this post we’ve included links to some of the main topics on the web site to help you get started. If there is a topic about which you would
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